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Alnylam B V — Amvuttra EMA EPAR public assessment report (EMEA/H/C/005852, 2022)

Alnylam B V · 2022 · EMA EPAR public assessment report · company profile →

Report summary

The EMA's public assessment report details the positive opinion for Alnylam's Amvuttra (vutrisiran) for adult patients with stage 1 or 2 hATTR amyloidosis polyneuropathy. The report covers the drug's quality, non-clinical profile, and clinical pharmacology, confirming its mechanism as a second-generation siRNA. The pivotal HELIOS-A study demonstrated significant improvements in neurological endpoints (mNIS+7, Norfolk QoL-DN, 10-MWT) and quality of life compared to placebo, and non-inferiority to patisiran in TTR reduction. Safety findings included common adverse events like injection site reactions, arthralgia, and dyspnoea, with no new major safety concerns identified. The overall benefit-risk balance was deemed positive.

Key findings — cited to the page

Incidence of Infusion Related Reactions (IRRs)10 (23.8%) n (%)HELIOS-A patisiran · p.154
Vutrisiran subjects with Grade 3 chronic kidney disease2 subjectsHELIOS-A · p.125
Patisiran subjects with Grade 3 chronic kidney disease3 subjectsHELIOS-A · p.125
All vutrisiran group subjects with Grade 3 abnormalities in coagulation parameters3 subjects · p.128
Vutrisiran patients with Grade 3 abnormalities in chemistry parameters4 patients · p.128
Vutrisiran subjects with Grade 3 haematology abnormalities2 subjects · p.127
Infusion related reactions (IRRs) incidence (patisiran)23.8 %HELIOS-A · p.120
Indicationtreatment of hereditary transthyretin-mediated amyloidosis (hATTR amyloidosis) in adult patients with stage 1 or stage 2 polyneuropathy Amvuttra (vutrisiran) · p.8
Marketing authorisation application submission date10 September 2021 Amvuttra (vutrisiran) · Europe · p.8
Clinical dose25 mgvutrisiran · p.41
CHMP positive opinion date21 July 2022 Amvuttra (vutrisiran) · p.10
Maximum recommended patisiran dose for patients ≥100 kg30 mgHELIOS-A · p.46

Source: Alnylam B V · License: EMA - reuse permitted with acknowledgement. Summary and findings are extracted from the published document; every figure cites its page. Informational only — not investment advice. Explore the Neurology library →

Alnylam B V — Amvuttra EMA EPAR public assessment report (EMEA/H/C/005852, 2022) — Summary & Key Findings | BioPharmaPT