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Ipsen S.A. — Ojemda EMA EPAR public assessment report (EMEA/H/C/006140, 2026)

Ipsen S.A. · 2026 · EMA EPAR public assessment report · company profile →

Report summary

The EMA granted a Conditional Marketing Authorisation for Ipsen's Ojemda (tovorafenib) for pediatric low-grade glioma (LGG) with BRAF fusions/rearrangements or V600 mutation, for patients aged 6 months and older who have progressed after prior systemic therapies. This decision, despite initial concerns about overlap with existing therapies and long-term safety, was based on promising efficacy and unmet medical need. Ojemda, available as tablets and oral suspension, is a RAF kinase inhibitor. Non-clinical studies detailed its mechanism, pharmacokinetics, and potential toxicities, including reproductive and phototoxicity risks. Clinical data from the FIREFLY-1 study in pediatric LGG patients showed an overall response rate of 52.6-53.9% and a median duration of response of 16.8-18.0 months. Safety analysis revealed a high incidence of adverse events, including Grade ≥3 TEAEs (81.8%), growth retardation, and specific concerns like hepatic and cardiac safety. Further data from the FIREFLY-2 study is deferred until 2030 to confirm long-term safety and efficacy.

Key findings — cited to the page

TEAEs Related to Study Drug with Severity Grade 3 or Higher for > 350 - 420 mg/m2 dose55.6 %FIREFLY-1 · p.107
TEAEs Related to Study Drug with Severity Grade 3 or Higher for > 420 mg/m2 dose74.6 %FIREFLY-1 · p.107
TEAEs with Severity Grade 3 or Higher for ≤ 350 mg/m2 dose73.3 %FIREFLY-1 · p.107
TEAEs Related to Study Drug with Severity Grade 3 or Higher for ≤ 350 mg/m2 dose66.7 %FIREFLY-1 · p.107
Rhinorrhoea (Any Grade)13.9 %FIREFLY-1 · p.108
Grade ≥ 3 TEAEs in FIREFLY-1 (Arm 1 + Arm 2)81.8 %FIREFLY-1 · p.106
Vomiting (Any Grade)56.2 %FIREFLY-1 · p.107
Fatal (Grade 5) TEAEs in FIREFLY-1 (Arm 1 + Arm 2)2.9 %FIREFLY-1 · p.106
TEAEs with Severity Grade 3 or Higher for > 350 - 420 mg/m2 dose74.6 %FIREFLY-1 · p.107
TEAEs with Severity Grade 3 or Higher for > 420 mg/m2 dose91.5 %FIREFLY-1 · p.107
Headache (Any Grade)52.6 %FIREFLY-1 · p.107
Hair colour changes (Any Grade)77.4 %FIREFLY-1 · p.107

Source: Ipsen S.A. · License: EMA - reuse permitted with acknowledgement. Summary and findings are extracted from the published document; every figure cites its page. Informational only — not investment advice. Explore the Oncology library →

Ipsen S.A. — Ojemda EMA EPAR public assessment report (EMEA/H/C/006140, 2026) — Summary & Key Findings | BioPharmaPT